About the disease

Signs and Symptoms

How attacks manifest and when it is a medical emergency.

HAE attacks are unpredictable and vary from patient to patient. They do not cause fever, except for a local temperature change in the case of subcutaneous attacks.

Subcutaneous attacks

  • Swelling in hands, feet, fingers, lips, eyelids, face, neck, chest, genitals
  • Redness with geographic pattern (prodromal signs)
  • Local warmth and tingling sensation
  • May restrict movement when affecting extremities

Abdominal attacks

  • Severe cramping pain
  • Nausea and vomiting
  • Occasional diarrhea
  • Caused by swelling of the intestinal walls
  • Symptoms similar to viral infections, food poisoning or appendicitis

Warning - medical emergency

Swelling in the face and/or neck can affect the upper respiratory tract and pose a life-threatening risk!

Edema in the throat, larynx or tongue can compromise the airway and constitutes a medical emergency.

Trigger factors

Swelling attacks occur spontaneously or are triggered by:

  • Physical trauma: Surgeries, dental procedures, sprains, dislocations, insect bites, high-impact exercise
  • Infections or inflammations
  • Hormonal changes: Menstruation, pregnancy, use of oral contraceptives
  • Emotional trauma: Stress, anxiety, worry
  • Medications: Estrogen-containing contraceptives, ACE inhibitors